pyruvate decarboxylase - definitie. Wat is pyruvate decarboxylase
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Wat (wie) is pyruvate decarboxylase - definitie


Pyruvate decarboxylase         
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CLASS OF ENZYMES
EC 4.1.1.1; 2-oxo-acid carboxy-lyase (aldehyde-forming)
Pyruvate decarboxylase is an enzyme () that catalyses the decarboxylation of pyruvic acid to acetaldehyde. It is also called 2-oxo-acid carboxylase, alpha-ketoacid carboxylase, and pyruvic decarboxylase.
Pyruvate dehydrogenase deficiency         
  • Citric acid cycle with aconitate 2
  • Glycolysis
  • Microcephaly and a normal head size
  • MRI of head(brain)- cerebral atrophy can be detected by such a method<ref name=emed/>
CARBOHYDRATE METABOLIC DISORDER CHARACTERIZED BY THE BUILDUP OF LACTIC ACID IN THE BODY AND A VARIETY OF NEUROLOGICAL PROBLEMS AND CAUSED BY A DEFICIENCY OF ONE OF THE THREE ENZYMES IN THE PYRUVATE DEHYDROGENASE COMPLEX
Pyruvate dehydrogenase complex deficiency disease; Deficiency of pyruvate dehydrogenase
Pyruvate dehydrogenase deficiency (also known as pyruvate dehydrogenase complex deficiency or PDCD) is a rare neurodegenerative disorders associated with abnormal mitochondrial metabolism. PDCD is a genetic disease resulting from mutations in one of the components of the pyruvate dehydrogenase complex (PDC).
Oxaloacetate decarboxylase         
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  • Oxaloacetate decarboxylase catalyzes the break down of oxaloacetate into pyruvate and carbon dioxide
CLASS OF ENZYMES
EC 4.1.1.3; Oxaloacetate carboxy-lyase (pyruvate-forming)
Oxaloacetate decarboxylase is a carboxy-lyase involved in the conversion of oxaloacetate into pyruvate.